HELP     Sign In

13q31.3CNV Type: Deletion-Duplication


Largest CNV size: 407254 bp

Statistics Box:
Number of Reports: 15



Summary Information

Summary statement in development

Additional Locus Information

Genome browsers

USCS Symbol             NCBI Symbol

Decipher

            Decipher Symbol

References

Major Reports

Title
Author, Year
Report Class
CNV Type
Structural variation of chromosomes in autism spectrum disorder.
Duplication
Functional impact of global rare copy number variation in autism spectrum disorders.
Deletion
De novo rates and selection of large copy number variation.
Deletion
An evidence-based approach to establish the functional and clinical significance of copy number variants in intellectual and developmental disabili...
Deletion
Post-axial polydactyly type A2, overgrowth and autistic traits associated with a chromosome 13q31.3 microduplication encompassing miR-17-92 and GPC5.
Duplication
Short stature, digit anomalies and dysmorphic facial features are associated with the duplication of miR-17~92 cluster.
Duplication
Identification of genetic causes of congenital neurodevelopmental disorders using genome wide molecular technologies.
Duplication

Minor Reports

Title
Author, Year
Report Class
CNV Type
Multiple recurrent de novo CNVs, including duplications of the 7q11.23 Williams syndrome region, are strongly associated with autism.
Deletion-Duplication
A discovery resource of rare copy number variations in individuals with autism spectrum disorder.
Deletion-Duplication
Refinement and discovery of new hotspots of copy-number variation associated with autism spectrum disorder.
Deletion
Both rare and de novo copy number variants are prevalent in agenesis of the corpus callosum but not in cerebellar hypoplasia or polymicrogyria.
Deletion
Performance of case-control rare copy number variation annotation in classification of autism.
Deletion-Duplication
Genome-wide analysis of copy number variations identifies PARK2 as a candidate gene for autism spectrum disorder.
Deletion
NA
Duplication
NA
Deletion

Cases

Cohort ID
Author, Year
Descripton
Cohort Size
Diagnosis
Age
Gender
CNV Size
Deletion
Duplication
Total CNV's
 chehbani_22_ASD_discovery_cases
  NA NA
 Patients recruited between January and April 2017 at the Child and Adolescent Psychiatry Clinic of the Department of Psychiatry, Fattouma Bourguiba University Hospital (Monastir, Tunisia); 91 patients were from simplex families, and 7 from multiplex families.
 98
 Clinical diagnosis of ASD based on DSM-IV and confirmed by ADI-R and ADOS.
 Range, 3-18 yrs.
 84.69% Male
 63042
 1
 0
 1
 egle_16_DD/ID_discovery_cases
 Patients assessed in the course of the Lithuanian-Swiss cooperation programme "Research and Development", the joint research project "Unique Genome Variants in Congenital Neurodevelopment Disorders: Origin, Genomic Mechanisms, Functional and Clinical Consequences" (UNIGENE)
 66
 All cases present with either syndromic or non-syndromic developmental delay/intellectual disability (DD/ID), ranging from mild to profound
 N/A
 N/A
 800000
 0
 1
 1
 engchuan_15_ASD_discovery_cases
 Samples from the Autism Genome Project (AGP)
 1892
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 N/A
 85.78% Male
 456885
 8
 3
 11
 girirajan_13a_ASD_discovery_cases
 1979 simplex cases from the Simons Simplex Collection (SSC), 579 multiplex cases from AGRE.
 2588
 Diagnosis of ASD based on meeting criteria on the Autism Diagnostic Observation Schedule (ADOS) and on the Autism Diagnostic Interview, Revised (ADI-R)
 NA
 NA
 76031
 1
 0
 1
 hemmat_14_ASD/DD/ADHD_discovery_cases
 9-year-old male proband from a pedigree with five maternal half-brothers presenting with autism and developmental delay; their mother also presented with developmental delay
 1
 Case presented with autism spectrum disorder (ASD), developmental delay (DD), speech delay, attention deficit hyperactivity disorder (ADHD), dysmorphic features, short stature, and digital abnormalities.
 9 yrs.
 Male
 516000
 0
 1
 1
 itsara_10_ASD_discovery_cases
 ASD probands from multiplex (n=1270) and simplex (n=60) families from AGRE collection
 1330
 ASD: Autism, broad spectrum autism (Spectrum), or NQA (not quite autism)
 
 
 65137
 1
 0
 1
 kaminsky_11_DD/ID/ASD_discovery_cases
 Cases from the International Standards for Cytogenomic Arrays (ISCA) consortium
 15749
 Unexplained developmental delay, intellectual disability, dysmorphic features, multiple congenital anomalies, autism spectrum disorders, or clinical features suggestive of a chromosomal syndrome
 NA
 NA
 2123578
 5
 0
 5
 kannu_13_DD/ASD_discovery_cases
 Male proband re-referred to genetics lab at age of 3 years for assessment of autism.
 1
 Developmental delay, autistic behavior, postaxial polydactyly, and overgrowth
 4.5 yrs.
 Male
 909500
 0
 1
 1
 larson_17_ASD_discovery_cases
  NA NA
 Participants with a dual diagnosis of ASD and psychosis that were recruited from clinical services in the public and independent sectors in the United Kingdom, as well as from charities and an Asperger's syndrome social networking website (study took place from January 2011 and April 2014)
 116
 All cases with a dual diagnosis of ASD and psychosis (affective, schizophrenic, and atypical)
 N/A
 N/A
 89455
 0
 1
 1
 marshall_08_ASD_discovery_cases
 Cohort of ASD families (237 simplex, 189 mulitplex) recruited from the Hospital for Sick Children, McMaster Univ., Memorial Univ., and other sites
 427
 ASD
 
 
 407254
 0
 3
 3
 pinto_10_ASD_discovery_cases
 Autism Genome Project (AGP) consortium patient cohort from families with at least two ASD individuals
 996
 ASD (ADI-R and ADOS): strict, broad, or spectrum ASD
 
 
 126859
 1
 0
 1
 prasad_12_ASD_discovery_cases
 Unrelated ASD cases recruited from three Canadian sites (Hospital for Sick Children, McMaster University, and Memorial University of Newfoundland); the majority of cases had been previously genotyped with results published in Marshall et al., 2008 and Pinto et al., 2010. 20 cases from initial cohort of 696 were excluded from further analysis (due to CNVs > 5 Mb).
 676
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS
 NA
 82.84% Male
 352931
 5
 5
 10
 sajan_13_ACC/CBLH/PMG_discovery_cases
 Individuals with severe congenital brain malformations [agenesis of the corpus callosum (ACC), cerebellar hypoplasia (CBLH), and/or polymicrogyria (PMG)] and additional neurodevelopmental phenotypes
 487
 Diagnosis of agenesis of the corpus callosum (ACC), cerebellar hypoplasia (CBLH), and/or polymicrogyria (PMG); additional diagnoses of autism spectrum disorder (ASD), developmental delay (DD), intellectual disability (ID) and/or seizures in some patients
 N/A
 N/A
 303879
 1
 0
 1
 sanders_11_ASD_discovery_cases
 Autistic probands from the Simons Simplex Collection (SSC). 872 probands in quartet families, 272 probands in trios.
 1124
 ASD diagnosis: 89.5% autism; 8.5% PDD-NOS, 2% Asperger syndrome. Mean full-scale IQ 85.1 1.5 (mean verbal IQ, 81.9 1.7; mean non-verbal IQ, 88.4 1.4)
 Mean, 9.1 yrs.
 86.1% Male
 357582
 1
 2
 3
 yin_16_ASD_discovery_cases
 Discovery cohort of ASD cases recruited from the Department of Psychiatry of National Taiwan University Hospital (NTUH), Chang Gung Memorial Hospital (CGMH), Taoyuan, and Taoyuan Mental Hospital (TMH), Taiwan.
 335
 Cases diagnosed with autistic disorder according to DSM-IV and confirmed by using the Chinese version of ADI-R. Cases' autistic behaviors assessed by Social Responsiveness Scale (SRS), and cognitive functions assessed by the Weschler Intelligence Scale for Children-Third Edition (WISC-III) and the Wisconsin Card Sorting Test (WCST).
 Mean, 9.39 4.04 yrs.
 89.3% Male
 5680
 1
 0
 1

Controls

Cohort ID
Author, Year
Descripton
Cohort Size
Diagnosis
Age
Gender
CNV Size
Deletion
Duplication
Total CNV's
 egle_16_DD/ID_discovery_controls
 CNVs from the Database of Genomic Variants (DGV)
 N/A
 Control
 N/A
 N/A
 0
 0
 0
 0
 engchuan_15_ASD_discovery_controls
 Platform-matched controls from three large studies: SAGE (Study of Addiction Genetics and Environment), Ontario Colorectal Cancer study, and HABC (Health Aging and Body Composition)
 2342
 Controls; subjects had no previous psychiatric history
 N/A
 46.67% Male
 464514
 5
 3
 8
 kaminsky_11_DD/ID/ASD_discovery_controls
 Controls from the International Standards for Cytogenomic Arrays (ISCA) consortium
 10118
 Controls
 NA
 NA
 NA
 NA
 NA
 NA
 larson_17_ASD_discovery_controls
  NA NA
 Entries listed in the Database of Genomic Variants (up to October 2017)
 N/A
 Control
 N/A
 N/A
 89455
 0
 1
 1
 marshall_08_ASD_discovery_controls_1
 German PopGen project and entries from Database of Genomic Variants
 500
 Controls
 
 
 0
 0
 0
 0
 marshall_08_ASD_discovery_controls_2
 Non-disease controls from Ontario population
 1152
 Controls
 
 
 0
 0
 0
 0
 prasad_12_ASD_discovery_controls
 PDx controls [1000 DNA samples from reportedly healthy donors (50.2% male) from BioServe (Beltsville, MD)] and 4139 in-house controls previously reported in Krawcak et al. 2006, Stewart et al. 2009, and Bierut et al. 2010. CNVs identified in controls were used to define rare ASD-specific CNVs.
 5139
 Control
 NA
 NA (PDx controls 50.2% male)
 352931
 0
 0
 0
 sanders_11_ASD_discovery_controls
 Matched siblings of autistic probands from the Simons Simplex Collection (SSC).
 872
 Controls
 Mean, 10.0 yrs.
 
 236768
 2
 1
 3
 yin_16_ASD_discovery_controls
 Individuals from the Han Chinese Cell and Genome Bank (HCCGB) in Taiwan
 1093
 Controls
 Mean, 68.07 10.12 yrs.
 48.0% Male
 5680
 0
 0
 0

Cases

Cohort ID
Geographical Ancestry
Discovery Method
Platform
Algorithm
Software
Validation Method
 chehbani_22_ASD_discovery_cases
  Tunisia
 aCGH
  Agilent SurePrint G3
 ADM-2
 Agilent Cytogenomic v.4.0.3.12.
 None
 egle_16_DD/ID_discovery_cases
  Lithuania
 aCGH
  Agilent 60K, Agilent 105K, or Agilent 1M
 ADM-2
 Feature Extraction 10.7.3.1, CytoGenomics 3.0.0.27 (Agilent)
 FISH or RT-PCR
 engchuan_15_ASD_discovery_cases
  Caucasian
 Solid phase hybridization
  Illumina 1M
 
 
 None
 girirajan_13a_ASD_discovery_cases
  NA
 aCGH
  Custom microarray with a high density of probes targeted to 1,367 regions with a susceptible genomic architecture
 ADM-2
 Agilent Genomic Workbench
 None
 hemmat_14_ASD/DD/ADHD_discovery_cases
  N/A
 Array SNP
  Affymetrix CytoScan HD
 
 Affymetrix ChAS v.2.0
 FISH
 itsara_10_ASD_discovery_cases
 
 Solid phase hybridization
  Illumina HumanHap550v1 and v3 SNP array
 HMM
 Illumina GenomeStudio
 aCGH (custom NimbleGen 12 X 135)
 kaminsky_11_DD/ID/ASD_discovery_cases
  NA
 aCGH
  Agilent 44K, Agilent 105K
 
 Feature Extraction, DNA Analytics
 FISH, qPCR, MLPA, aCGH, standard G-banded chromosome analysis
 kannu_13_DD/ASD_discovery_cases
  Caucasian
 aCGH
  SignatureChipOS 105K array (Agilent)
 
 
 aCGH, QMPSF
 larson_17_ASD_discovery_cases
  United Kingdom
 Array SNP
  Affymetrix CytoScan HD 2.8M, Affymetrix Cytogenetics
 SNP-FASST2 Segmentation
 Nexus Copy Number 7 (BioDiscovery), Affymetrix ChAS
 None
 marshall_08_ASD_discovery_cases
  90% European, 4.5% European-mixed, 4.5% Asian, 0.07% African
 Array SNP, karotyping
  Affymetrix 500K
 dChip, CNAG, GEMCA
 
 qPCR, qmPCR
 pinto_10_ASD_discovery_cases
  European
 Solid phase hybridization
  Illumina Infinium 1M SNP microarray
 QuantiSNP, iPattern
 
 qPCR, long-range PCR (LR-PCR), MLPA, FISH, aCGH (Agilent 1M), array SNP (Affymetrix 500K)
 prasad_12_ASD_discovery_cases
  Canada
 aCGH
  Agilent 1M
 ADM-2, DNAcopy (R Bioconductor)
 DNA Analytics v4.0.85 (Agilent), DNAcopy
 None
 sajan_13_ACC/CBLH/PMG_discovery_cases
  81.31% Caucasian
 Solid phase hybridization
  Illumina InfiniumII HumanHap610
 PennCNV
 
 None (not tested or failure to confirm by qPCR)
 sanders_11_ASD_discovery_cases
  White non-Hispanic, 74.5%; mixed, 9.3%, Asian, 4.3%, White Hispanic, 4.0%, African-American, 3.8%; other, 4.2&
 Solid phase hybridization
  Illumina 1M v1, Illumina 1M v3
 PennCNV, QuantiSNP, GNOSIS
 
 
 yin_16_ASD_discovery_cases
  Han Chinese
 Array SNP
  Affymetrix 6.0
 
 Affymetrix Genotyping Console v.4.1
 None

Controls

Cohort ID
Geographical Ancestry
Discovery Method
Platform
Algorithm
Software
Validation Method
  egle_16_DD/ID_discovery_controls
  N/A
  N/A
  N/A
 
 
 
  engchuan_15_ASD_discovery_controls
  Caucasian
  Solid phase hybridization
  Illumina 1M
 
 
  None
  kaminsky_11_DD/ID/ASD_discovery_controls
  NA
  aCGH
  Agilent 44K, Agilent 105K
 
  Feature Extraction, DNA Analytics
 
  larson_17_ASD_discovery_controls
  N/A
  N/A
  N/A
 
 
 
  marshall_08_ASD_discovery_controls_1
  European
  Array SNP, karotyping
  Affymetrix 500K
  dChip, CNAG, GEMCA
 
 
  marshall_08_ASD_discovery_controls_2
  European
  Array SNP, karotyping
  Affymetrix 500K
  dChip, CNAG, GEMCA
 
 
  prasad_12_ASD_discovery_controls
  NA
  aCGH
  Agilent 1M
  ADM-2, DNAcopy (R Bioconductor)
  DNA Analytics v4.0.85 (Agilent), DNAcopy
 
  sanders_11_ASD_discovery_controls
 
  Solid phase hybridization
  Illumina 1M v1 or Illumina 1M v3
  PennCNV, QuantiSNP, GNOSIS
 
 
  yin_16_ASD_discovery_controls
  Han Chinese
  Array SNP
  Affymetrix 6.0
 
  Affymetrix Genotyping Console v.4.1
  None

Cases

Patient ID
Author, Year
Age
Gender
Primary Diagnosis
Clinical Profile
Cognitive Profile
CNV Start
CNV End
CNV Size
Genome Build
Type Method
Validation
  chehbani_22_ASD_discovery_cases-case21
  NA NA
 NA
 F
 ASD
 Case diagnosed with ASD based on DSM-IV criteria and confirmed by ADI-R and ADOS-2.
 
 93667350
 93730391
  63042
 GRCh38
 Deletion
 No
  egle_16_DD/ID_discovery_cases-case14_1
 19 yrs.
 F
 Intellectual disability
 Arnold-Chiari deformation, strabismus, nystagmus, tall stature, facial asymmetry, arachnodactyly, rough hair
 Intellectual disability
 90514494
 91358647
  844154
 GRCh38
 Duplication
 Yes
  engchuan_15_ASD_discovery_cases-case2201_1
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 92953830
 93034129
  80300
 GRCh38
 Deletion
 No
  engchuan_15_ASD_discovery_cases-case3148_4
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 93916025
 94010796
  94772
 GRCh38
 Deletion
 No
  engchuan_15_ASD_discovery_cases-case3429_3
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 89829165
 89992703
  163539
 GRCh38
 Deletion
 No
  engchuan_15_ASD_discovery_cases-case4255_1
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 89776939
 90233824
  456886
 GRCh38
 Deletion
 No
  engchuan_15_ASD_discovery_cases-case4418_1
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 93496629
 93540099
  43471
 GRCh38
 Deletion
 No
  engchuan_15_ASD_discovery_cases-case4420_1
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 93382681
 93544963
  162283
 GRCh38
 Deletion
 No
  engchuan_15_ASD_discovery_cases-case4508_1
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 94323534
 94371977
  48444
 GRCh38
 Duplication
 No
  engchuan_15_ASD_discovery_cases-case5115_3
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 94137490
 94264348
  126859
 GRCh38
 Deletion
 No
  engchuan_15_ASD_discovery_cases-case5291_4
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 89807811
 89866658
  58848
 GRCh38
 Duplication
 No
  engchuan_15_ASD_discovery_cases-case5355_3
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 91511103
 91616592
  105490
 GRCh38
 Duplication
 No
  engchuan_15_ASD_discovery_cases-case8472_201
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 91039773
 91155826
  116054
 GRCh38
 Deletion
 No
  girirajan_13a_ASD_discovery_cases-AU1165302
 N/A
 N/A
 ASD
 Diagnosis of ASD based on meeting criteria on the Autism Diagnostic Observation Schedule (ADOS) and on the Autism Diagnostic Interview, Revised (ADI-R)
 N/A
 94024844
 94100875
  76032
 GRCh38
 Deletion
 No
  hemmat_14_ASD/DD/ADHD_discovery_cases-case1
 9 yrs.
 M
 ASD, DD, and ADHD
 Birth/neonatal history: born at full term via vaginal delivery to a G4P4A0L4 25-year-old mother without any known maternal complications or infections; birth weight of 3580 g; no prenatal, perinatal, or postnatal complications noted. Developmental milestones: walking at 12 months; did not speak words until age of 3 years. Language and communication evaluation: speech delay. Motor and musculoskeletal evaluation: metacarpal and metatarsal anomalies, flat feet, lower facial weakness; digit anomalies including brachydactyly, wide nail beds, deviation of fourth digits to the ulnar side, radially displaced thumbs, mild clinodactyly; hand breadth, hand length, and hand circumference were <1% for age and gender. Behavioral/psychiatric evaluation: autism spectrum disorder, attention deficit hyperactivity disorder. Dysmorphic features: hypertelorism, downward slanting palpebral fissures, frequent dental caries. Growth parameters: short stature (10th %ile), mild macrocephaly in relation to body size. Family history: mother with short stature, digital abnormalities, and developmental delay (positive for 13q31.3 duplication); case had five half-brothers resulting from his mother's four different marriages, all of whom reported to exhibit developmental delay and autism; one half-brother also presented with short stature and digital abnormalities.
 Developmental delay; interventions included speech and physical therapy, an individualized education plan, and special education for diagnoses of developmental delay and ASD.
 91337007
 91852603
  515597
 GRCh38
 Duplication
 Yes
  itsara_10_ASD_discovery_cases-HI1493
 NA
 NA
 Autism
 NA
 NA
 90300119
 90365256
  65138
 GRCh38
 Deletion
 Yes
  kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00000244
 NA
 NA
 Developmental delay/intellectual disability/ASD
 Clinical profile NA
 Cognitive profile NA
 91615056
 91879009
  263954
 GRCh38
 Deletion
 Yes
  kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00001622
 NA
 NA
 Developmental delay/intellectual disability/ASD
 Clinical profile NA
 Cognitive profile NA
 90973752
 93097331
  2123580
 GRCh38
 Deletion
 Yes
  kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00003974
 NA
 NA
 Developmental delay/intellectual disability/ASD
 Clinical profile NA
 Cognitive profile NA
 90215412
 91366486
  1151075
 GRCh38
 Deletion
 Yes
  kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00004338
 NA
 NA
 Developmental delay/intellectual disability/ASD
 Clinical profile NA
 Cognitive profile NA
 91431897
 91628212
  196316
 GRCh38
 Deletion
 Yes
  kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00005097
 NA
 NA
 Developmental delay/intellectual disability/ASD
 Clinical profile NA
 Cognitive profile NA
 93345058
 93629454
  284397
 GRCh38
 Deletion
 Yes
  kannu_13_DD/ASD_discovery_cases-case1
 4.5 yrs.
 M
 Developmental delay and autistic behavior
 Case re-referred at age of 3 years for assessment of autism (no formal diagnosis of ASD noted). Birth/neonatal history: born at 33 weeks 3 days gestation by C-section; pregnancy complicated by type II diabetes, hypertension, and oligohydramnios; mother (41 years old at time of delivery) given single dose of corticosteroids prior to delivery; birth weight of 1813 g (25th %ile), lenght of 40 cm (3rd %ile), and head circumference of 32 cm (25th %ile); telecanthus and bilateral postaxial polydactyly (which was later ligated) noted; cranial ultrasound revealed right choroid plexus cyst; echocardiogram disclosed patent ductus ateriosis and two small secundum atrial septal defects; normal male karyotype (46, XY), 22q11.2 microdeletion excluded by FISH analysis; neonatal course otherwise relatively benign. Developmental milestones: development concerns noted at age of 11 months (slept poorly at night, did not vocalize); formal developmental assessment at age of 2 years suggested autistic behavior and developmental delay; non-verbal and did not use gestures to communicate; delays in gross motor development (difficulties in climbing stairs, running, throwing, or catching a ball). Language and communication evaluation: few single words in vocabulary. Behavioral/psychiatric evaluation: autistic behavior suggested at age of 2 years; preferred playing by himself, easily upset by other children, easily startled by sound, adapted poorly to change, failure to respond to name, failure to demonstrate stranger anxiety or imitation skills. Brain imaging: cerebral MRI at age of 4 years showed no structural brain abnormalities. Other medical history: bilateral inguinal hernia surgery at age of 2 years 11 months; recurrent wheeze with respiratory infections. Dysmorphic features: prominent, posteriorly-rotated, low-set ears, bilateral epicanthic folds, up-slanting palpebral fissures, prominent teeth, high-arched palate, prominent jaw. Growth parameters: weight of 17.1 kg (75th-90th %ile), height of 116 cm (>97th %ile), and OFC of 51 cm (10th %ile) at age of 4.5 years. Family history: one of a sibship of two (21-year-old sibling is healthy and does not carry 13q31.3 duplication); mother with history of post-axial polydactyly (ligated as neonate), social awkwardness and mood disorder.
 Developmental delay; case making slow progress with development at age of 4.5 years.
 90867746
 91777746
  910001
 GRCh38
 Duplication
 Yes
  larson_17_ASD_discovery_cases-case88
  NA NA
 N/A
 N/A
 ASD and psychosis
 No additional clinical information available. Patient carries CNV that is present in DGV (less than 1.5%) but was not present in 1124 ASD cases without psychosis from the Simons Simplex Collection.
 
 92306848
 92396303
  89456
 GRCh38
 Duplication
 No
  marshall_08_ASD_discovery_cases-NA0048-000
 NA
 M
 ASD
 NA
 NA
 93838266
 93894346
  56081
 GRCh38
 Duplication
 Yes
  marshall_08_ASD_discovery_cases-SK0326-003
 NA
 M
 ASD
 NA
 NA
 94047145
 94282676
  235532
 GRCh38
 Duplication
 Yes
  marshall_08_ASD_discovery_cases-SK0326-003
 NA
 M
 ASD
 NA
 NA
 90276711
 90683964
  407254
 GRCh38
 Duplication
 Yes
  pinto_10_ASD_discovery_cases-case5115_3
 NA
 M
 ASD
 NA
 NA
 94137490
 94264348
  126859
 GRCh38
 Deletion
 Yes
  prasad_12_ASD_discovery_cases-case102830
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. CNV identified by previous SNP microarray study
 
 90958823
 91067952
  109130
 Unknown
 Duplication
 No
  prasad_12_ASD_discovery_cases-case110953
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. Novel CNV
 
 89661145
 89665867
  4723
 Unknown
 Duplication
 No
  prasad_12_ASD_discovery_cases-case138145L
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. CNV identified by previous SNP microarray study
 
 91325119
 91347213
  22095
 Unknown
 Deletion
 No
  prasad_12_ASD_discovery_cases-case146442L
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. CNV identified by previous SNP microarray study
 
 91146602
 91160878
  14277
 Unknown
 Deletion
 No
  prasad_12_ASD_discovery_cases-case146449L
 NA
 F
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. Novel CNV
 
 88810171
 88818771
  8601
 Unknown
 Deletion
 No
  prasad_12_ASD_discovery_cases-case55634
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. CNV identified by previous SNP microarray study
 
 89255637
 89314434
  58798
 Unknown
 Duplication
 No
  prasad_12_ASD_discovery_cases-case81155
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. CNV identified by previous SNP microarray study
 
 93509199
 93721180
  211982
 Unknown
 Duplication
 No
  prasad_12_ASD_discovery_cases-case81155
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. CNV identified by previous SNP microarray study
 
 89732291
 90085221
  352931
 Unknown
 Duplication
 No
  prasad_12_ASD_discovery_cases-caseL879
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. Novel CNV
 
 92194931
 92202851
  7921
 Unknown
 Deletion
 No
  prasad_12_ASD_discovery_cases-caseMM0234-5
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. CNV identified by previous SNP microarray study
 
 93594054
 93714629
  120576
 Unknown
 Deletion
 No
  sajan_13_ACC/CBLH/PMG_discovery_cases-case1303-0
 N/A
 N/A
 ACC-PMG
 Diagnosis of agenesis of the corpus callosum (ACC) and polymicrogyria (PMG). ASD: no. Seizures: no.
 Developmental delay: yes. Intellectual disability: yes.
 93470922
 93774800
  303879
 GRCh38
 Deletion
 No
  sanders_11_ASD_discovery_cases-11284.p1
 8.3
 M
 ASD
 NA
 Full-scale IQ, 122; non-verbal IQ, 117; verbal IQ, 125
 89764094
 89838629
  74536
 GRCh38
 Duplication
 No
  sanders_11_ASD_discovery_cases-11522.p1
 11.3
 M
 Autism
 NA
 Full-scale IQ, 67; non-verbal IQ, 79; verbal IQ, 60
 90756385
 90805005
  48621
 GRCh38
 Deletion
 No
  sanders_11_ASD_discovery_cases-11868.p1
 7.9
 M
 Autism
 NA
 Full-scale IQ, 88; non-verbal IQ, 91; verbal IQ, 86
 92019615
 92377197
  357583
 GRCh38
 Duplication
 No
  yin_16_ASD_discovery_cases-case451
 N/A
 N/A
 ASD
 Cases diagnosed with autistic disorder according to DSM-IV and confirmed by using the Chinese version of ADI-R.
 
 92387559
 92393238
  5680
 GRCh38
 Deletion
 No

Controls

Patient ID
Author, Year
Age
Gender
Primary Diagnosis
Clinical Profile
Cognitive Profile
CNV Start
CNV End
CNV Size
Genome Build
Type Method
Validation
  engchuan_15_ASD_discovery_controls-control110036004877_
  N/A
  N/A
  Control
  No previous psychiatric history
 
  89769310
  90233824
  464515
  GRCh38
  Deletion
  No
  engchuan_15_ASD_discovery_controls-controlB742876_1007852892
  N/A
  N/A
  Control
  No previous psychiatric history
 
  91409624
  91649607
  239984
  GRCh38
  Deletion
  No
  engchuan_15_ASD_discovery_controls-controlB776367_1007875364
  N/A
  N/A
  Control
  No previous psychiatric history
 
  92308440
  92391120
  82681
  GRCh38
  Duplication
  No
  engchuan_15_ASD_discovery_controls-controlHABC_900157_900157
  N/A
  N/A
  Control
  No previous psychiatric history
 
  91977218
  92202881
  225664
  GRCh38
  Duplication
  No
  engchuan_15_ASD_discovery_controls-controlHABC_900157_900157
  N/A
  N/A
  Control
  No previous psychiatric history
 
  92246199
  92516160
  269962
  GRCh38
  Duplication
  No
  engchuan_15_ASD_discovery_controls-controlHABC_900839_900839
  N/A
  N/A
  Control
  No previous psychiatric history
 
  92632408
  92698970
  66563
  GRCh38
  Deletion
  No
  engchuan_15_ASD_discovery_controls-controlHABC_900904_900904
  N/A
  N/A
  Control
  No previous psychiatric history
 
  91409624
  91649607
  239984
  GRCh38
  Deletion
  No
  engchuan_15_ASD_discovery_controls-controlHABC_901214_901214
  N/A
  N/A
  Control
  No previous psychiatric history
 
  89769310
  90233824
  464515
  GRCh38
  Deletion
  No
  sanders_11_ASD_discovery_controls-11284.s1
  7.1
  F
  Control (matched sibling)
  NA
  NA
  89764094
  89838629
  74536
  GRCh38
  Duplication
  No
  sanders_11_ASD_discovery_controls-11522.s1
  15.6
  M
  Control (matched sibling)
  NA
  NA
  90756385
  90804614
  48230
  GRCh38
  Deletion
  No
  sanders_11_ASD_discovery_controls-11843.s1
  16.9
  F
  Control (matched sibling)
  NA
  NA
  91412839
  91649607
  236769
  GRCh38
  Deletion
  No

Cases

Patient ID
Validation Description
Primary Disorder Inheritence
Inheritence
Family Profile
Disease Segregation
Gene Content
Altered Gene Expression
 chehbani_22_ASD_discovery_cases-case21
 
 
 Unknown
 Simplex
 
 GPC6
 
 egle_16_DD/ID_discovery_cases-case14_1
 FISH or RT-PCR
 
 De novo
 
 
 RNU6-75P,BRK1P2,LINC00380,PPIAP23,MIR17HG,MIR17,MIR18A,MIR19A,MIR20A,MIR19B1,MIR92A1,LINC01049,LINC00410,LINC00379
 
 engchuan_15_ASD_discovery_cases-case2201_1
 
 
 Unknown
 
 
 
 
 engchuan_15_ASD_discovery_cases-case3148_4
 
 
 Unknown
 
 
 GPC6
 
 engchuan_15_ASD_discovery_cases-case3429_3
 
 
 Unknown
 
 
 PEX12P1,RPL7L1P1
 
 engchuan_15_ASD_discovery_cases-case4255_1
 
 
 Unknown
 
 
 PEX12P1,RNA5SP34,FAR1P1,KRT18P27,MIR622,RPL7L1P1,LINC00559
 
 engchuan_15_ASD_discovery_cases-case4418_1
 
 
 Unknown
 
 
 GPC6
 
 engchuan_15_ASD_discovery_cases-case4420_1
 
 
 Unknown
 
 
 HNRNPA1P29,GPC6
 
 engchuan_15_ASD_discovery_cases-case4508_1
 
 
 Unknown
 
 
 GPC6
 
 engchuan_15_ASD_discovery_cases-case5115_3
 
 
 Unknown
 
 
 GPC6-AS1,GPC6
 
 engchuan_15_ASD_discovery_cases-case5291_4
 
 
 Unknown
 
 
 RPL7L1P1
 
 engchuan_15_ASD_discovery_cases-case5355_3
 
 
 Unknown
 
 
 GPC5
 
 engchuan_15_ASD_discovery_cases-case8472_201
 
 
 Unknown
 
 
 LINC00380,LINC00379
 
 girirajan_13a_ASD_discovery_cases-AU1165302
 
 
 Unknown
 Multiplex
 Unknown
 RNA5SP35,GPC6
 
 hemmat_14_ASD/DD/ADHD_discovery_cases-case1
 FISH
 Possibly maternal
 Maternal
 Multiplex
 Not segregated (not all ASD-affected siblings carry 13q31.3 duplication)
 MIR17HG,MIR17,MIR18A,MIR19A,MIR20A,MIR19B1,MIR92A1,GPC5
 
 itsara_10_ASD_discovery_cases-HI1493
 aCGH (custom NimbleGen 12 X 135)
 
 De novo
 Multiplex
 
 
 
 kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00000244
 FISH, qPCR, MLPA, aCGH, or standard G-banded chromosome analysis
 
 Unknown
 Unknown
 Unknown
 GPC5
 
 kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00001622
 FISH, qPCR, MLPA, aCGH, or standard G-banded chromosome analysis
 
 Maternal
 Unknown
 Unknown
 BRK1P2,LINC00380,PPIAP23,MIR17HG,MIR17,MIR18A,MIR19A,MIR20A,MIR19B1,MIR92A1,RNU4ATAC3P,FABP5P4,MIR548AS,LINC00363,LINC00379,GPC5-AS2,GPC5-IT1,GPC5-AS1,GPC5
 
 kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00003974
 FISH, qPCR, MLPA, aCGH, or standard G-banded chromosome analysis
 
 De novo
 Unknown
 Unknown
 KRT18P27,MIR622,RNU6-75P,BRK1P2,LINC00380,PPIAP23,MIR17HG,MIR17,MIR18A,MIR19A,MIR20A,MIR19B1,MIR92A1,LINC01049,LINC00410,LINC00379
 
 kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00004338
 FISH, qPCR, MLPA, aCGH, or standard G-banded chromosome analysis
 
 Unknown
 Unknown
 Unknown
 GPC5
 
 kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00005097
 FISH, qPCR, MLPA, aCGH, or standard G-banded chromosome analysis
 
 Unknown
 Unknown
 Unknown
 HNRNPA1P29,GPC6
 
 kannu_13_DD/ASD_discovery_cases-case1
 aCGH, QMPSF
 Maternal
 Maternal
 Possibly multi-generational
 Segregated
 BRK1P2,LINC00380,PPIAP23,MIR17HG,MIR17,MIR18A,MIR19A,MIR20A,MIR19B1,MIR92A1,LINC00410,LINC00379,GPC5
 
 larson_17_ASD_discovery_cases-case88
 
 
 Unknown
 
 Unknown
 GPC5-AS2,GPC5
 
 marshall_08_ASD_discovery_cases-NA0048-000
 qPCR, qmPCR
 
 Unknown
 NA
 NA
 GPC6
 
 marshall_08_ASD_discovery_cases-SK0326-003
 qPCR, qmPCR
 
 Unknown
 NA
 NA
 GPC6-AS1,GPC6
 
 marshall_08_ASD_discovery_cases-SK0326-003
 qPCR, qmPCR
 
 Unknown
 NA
 NA
 LINC01049
 
 pinto_10_ASD_discovery_cases-case5115_3
 Agilent1M
 
 paternal
 NA
 NA
 GPC6-AS1,GPC6
 
 prasad_12_ASD_discovery_cases-case102830
 
 
 Unknown
 Unknown
 Unknown
 GPC5
 
 prasad_12_ASD_discovery_cases-case110953
 
 
 Unknown
 Unknown
 Unknown
 0 genes
 
 prasad_12_ASD_discovery_cases-case138145L
 
 
 Unknown
 Unknown
 Unknown
 GPC5
 
 prasad_12_ASD_discovery_cases-case146442L
 
 
 Unknown
 Unknown
 Unknown
 GPC5
 
 prasad_12_ASD_discovery_cases-case146449L
 
 
 Unknown
 Unknown
 Unknown
 0 genes
 
 prasad_12_ASD_discovery_cases-case55634
 
 
 Unknown
 Unknown
 Unknown
 0 genes
 
 prasad_12_ASD_discovery_cases-case81155
 
 
 Unknown
 Unknown
 Unknown
 GPC6
 
 prasad_12_ASD_discovery_cases-case81155
 
 
 Unknown
 Unknown
 Unknown
 0 genes
 
 prasad_12_ASD_discovery_cases-caseL879
 
 
 Unknown
 Unknown
 Unknown
 GPC5
 
 prasad_12_ASD_discovery_cases-caseMM0234-5
 
 
 Unknown
 Unknown
 Unknown
 GPC6
 
 sajan_13_ACC/CBLH/PMG_discovery_cases-case1303-0
 Not tested by qPCR
 
 Unknown
 Unknown
 Unknown
 GPC6
 
 sanders_11_ASD_discovery_cases-11284.p1
 
 
 Maternal
 Simplex (quad-proband matched)
 Not segregated
 RPL7L1P1
 
 sanders_11_ASD_discovery_cases-11522.p1
 
 
 Paternal
 Simplex (quad-proband matched)
 Not segregated
 RNU6-75P
 
 sanders_11_ASD_discovery_cases-11868.p1
 
 
 Maternal
 Simplex (quad-proband matched)
 Not segregated
 RNU4ATAC3P,FABP5P4,GPC5-AS2,GPC5
 
 yin_16_ASD_discovery_cases-case451
 
 
 Unknown
 Unknown
 Unknown
 GPC5
 

Controls

Patient ID
Validation Description
Primary Disorder Inheritence
Inheritence
Family Profile
Disease Segregation
Gene Content
Altered Gene Expression
engchuan_15_ASD_discovery_controls-control110036004877_
 
 
  Unknown
 
 
  PEX12P1,RNA5SP34,FAR1P1,KRT18P27,MIR622,RPL7L1P1,LINC00559
 
engchuan_15_ASD_discovery_controls-controlB742876_1007852892
 
 
  Unknown
 
 
  GPC5
 
engchuan_15_ASD_discovery_controls-controlB776367_1007875364
 
 
  Unknown
 
 
  GPC5-AS2,GPC5
 
engchuan_15_ASD_discovery_controls-controlHABC_900157_900157
 
 
  Unknown
 
 
  RNU4ATAC3P,FABP5P4,GPC5
 
engchuan_15_ASD_discovery_controls-controlHABC_900157_900157
 
 
  Unknown
 
 
  MIR548AS,GPC5-AS2,GPC5-IT1,GPC5
 
engchuan_15_ASD_discovery_controls-controlHABC_900839_900839
 
 
  Unknown
 
 
  GPC5
 
engchuan_15_ASD_discovery_controls-controlHABC_900904_900904
 
 
  Unknown
 
 
  GPC5
 
engchuan_15_ASD_discovery_controls-controlHABC_901214_901214
 
 
  Unknown
 
 
  PEX12P1,RNA5SP34,FAR1P1,KRT18P27,MIR622,RPL7L1P1,LINC00559
 
sanders_11_ASD_discovery_controls-11284.s1
 
 
  Maternal
  Simplex (quad)
  NA
  RPL7L1P1
 
sanders_11_ASD_discovery_controls-11522.s1
 
 
  Paternal
  Simplex (quad)
  NA
  RNU6-75P
 
sanders_11_ASD_discovery_controls-11843.s1
 
 
  Paternal
  Simplex (quad)
  NA
  GPC5
 

No Animal Model Data Available
HELP
Copyright © 2017 MindSpec, Inc.