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7q32.3CNV Type: Deletion


Largest CNV size: 5598 bp

Statistics Box:
Number of Reports: 7



Summary Information

Summary statement in development

Additional Locus Information

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USCS Symbol             NCBI Symbol

Decipher

            Decipher Symbol

References

Major Reports

Title
Author, Year
Report Class
CNV Type
A discovery resource of rare copy number variations in individuals with autism spectrum disorder.
Deletion-Duplication
Targeted resequencing of 358 candidate genes for autism spectrum disorder in a Chinese cohort reveals diagnostic potential and genotype-phenotype c...
Duplication

Minor Reports

Title
Author, Year
Report Class
CNV Type
Multiple recurrent de novo CNVs, including duplications of the 7q11.23 Williams syndrome region, are strongly associated with autism.
Deletion
Genome wide analysis in a family with sensorineural hearing loss, autism and mental retardation.
Deletion
Performance of case-control rare copy number variation annotation in classification of autism.
Duplication
RYR2, PTDSS1 and AREG genes are implicated in a Lebanese population-based study of copy number variation in autism.
Duplication
Paternally inherited cis-regulatory structural variants are associated with autism.
Deletion

Cases

Cohort ID
Author, Year
Descripton
Cohort Size
Diagnosis
Age
Gender
CNV Size
Deletion
Duplication
Total CNV's
 brandler_18_ASD_replication_cases
 Affected individuals from MSSNG cohort (1395 cases from 1187 families) and the Simons Simplex 2 (SSC2) cohort (584 cases from simplex quad families)
 1979
 Cases diagnosed with ASD
 N/A
 N/A
 139775
 3
 0
 3
 engchuan_15_ASD_discovery_cases
 Samples from the Autism Genome Project (AGP)
 1892
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 N/A
 85.78% Male
 308967
 0
 1
 1
 mosrati_12_ASD/MR_discovery_cases
 Affected siblings from a consanguineous Tunisian family with moderate to profound congenital hearing loss associated with mental retardation and autistic behavior.
 3
 Congenital hearing loss (3/3), mental retardation (2/3), and autistic traits (2/3)
 Range, 22-31 yrs.
 66.67% Male
 247488
 1
 0
 1
 prasad_12_ASD_discovery_cases
 Unrelated ASD cases recruited from three Canadian sites (Hospital for Sick Children, McMaster University, and Memorial University of Newfoundland); the majority of cases had been previously genotyped with results published in Marshall et al., 2008 and Pinto et al., 2010. 20 cases from initial cohort of 696 were excluded from further analysis (due to CNVs > 5 Mb).
 676
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS
 NA
 82.84% Male
 111960
 1
 2
 3
 sanders_11_ASD_discovery_cases
 Autistic probands from the Simons Simplex Collection (SSC). 872 probands in quartet families, 272 probands in trios.
 1124
 ASD diagnosis: 89.5% autism; 8.5% PDD-NOS, 2% Asperger syndrome. Mean full-scale IQ 85.1 1.5 (mean verbal IQ, 81.9 1.7; mean non-verbal IQ, 88.4 1.4)
 Mean, 9.1 yrs.
 86.1% Male
 5598
 4
 0
 4
 soueid_16_ASD_discovery_cases
 Autistic children; 37/41 from 35 fully analyzed families (33 simplex, 2 multiplex)
 41
 All cases fulfilled DSM-V criteria for autism
 Range, 3-18 yrs.
 92.68% Male
 646000
 0
 1
 1
 soueid_16_DD/ID_discovery_cases
 Individuals referred to clinical neurogenetics service with non-syndromic developmental delay and intellectual disabilities (DD/ID) or rare neurological syndromes
 35
 Cases present with non-syndromic developmental delay and intellectual disabilities (DD/ID) or rare neurological syndromes
 N/A
 N/A
 0
 0
 0
 0
 zhou_19_ASD_discovery_cases
 ASD probands from families recruited from training centers in Beijing and Tsingdao, China
 539
 Cases were diagnosed for ASD by ADI-R and ADOS
 4.92 1.20 years
 87.38% Male
 79000
 0
 2
 2

Controls

Cohort ID
Author, Year
Descripton
Cohort Size
Diagnosis
Age
Gender
CNV Size
Deletion
Duplication
Total CNV's
 brandler_18_ASD_discovery_controls
 Unaffected individuals from the Relating Genes with Adolescent and Child Health (REACH) cohort (112 individuals from 311 families) and the Simons Simplex 1 (SSC1) cohort (518 controls from simplex quad families)
 630
 Control
 N/A
 N/A
 897
 1
 0
 1
 engchuan_15_ASD_discovery_controls
 Platform-matched controls from three large studies: SAGE (Study of Addiction Genetics and Environment), Ontario Colorectal Cancer study, and HABC (Health Aging and Body Composition)
 2342
 Controls; subjects had no previous psychiatric history
 N/A
 46.67% Male
 644044
 0
 2
 2
 krumm_15_ASD_discovery_controls
 Unaffected siblings from quad families from the Simons Simplex Collection
 1786
 Control
 N/A
 N/A
 7621
 0
 1
 1
 levy_11_ASD_discovery_controls
 Unaffected siblings of autistic probands from 887 families from the Simons Simplex Collection (SSC)
 863
 Control
 
 47.97% Male
 91304
 0
 1
 1
 prasad_12_ASD_discovery_controls
 PDx controls [1000 DNA samples from reportedly healthy donors (50.2% male) from BioServe (Beltsville, MD)] and 4139 in-house controls previously reported in Krawcak et al. 2006, Stewart et al. 2009, and Bierut et al. 2010. CNVs identified in controls were used to define rare ASD-specific CNVs.
 5139
 Control
 NA
 NA (PDx controls 50.2% male)
 15521
 0
 2
 2
 sanders_11_ASD_discovery_controls
 Matched siblings of autistic probands from the Simons Simplex Collection (SSC).
 872
 Controls
 Mean, 10.0 yrs.
 
 54127
 1
 1
 2
 soueid_16_ASD_discovery_controls
 Control cohort of normal participants
 37
 Control
 N/A
 51.35% Male
 0
 0
 0
 0
 zhou_19_ASD_discovery_controls
 Samples from blood donors at donation stations in Beijing, China (note: CNVs identified in controls not reported in this study)
 512
 Controls were screened for ASD by AQ measurement (score < 32) and self-reported to be negative for personal or family history of neurological disorders or psychiatric illness related to ASD and adverse pregnancy history
 29.77 9.12 years
 76.17% Male
 N/A
 N/A
 N/A
 N/A

Cases

Cohort ID
Geographical Ancestry
Discovery Method
Platform
Algorithm
Software
Validation Method
 brandler_18_ASD_replication_cases
  N/A
 WGS
  Illumina HiSeq X10
 ForestSV, Lumpy, Manta, Mobster, SV2
 
 None
 engchuan_15_ASD_discovery_cases
  Caucasian
 Solid phase hybridization
  Illumina 1M
 
 
 None
 mosrati_12_ASD/MR_discovery_cases
  Tunisian
 Solid phase hybridization
  Illumina HumanCyto12v2.0 BeadChip
 QuantiSNP, PennCNV, VanillaICE
 BeadStudio V3.3
 None
 prasad_12_ASD_discovery_cases
  Canada
 aCGH
  Agilent 1M
 ADM-2, DNAcopy (R Bioconductor)
 DNA Analytics v4.0.85 (Agilent), DNAcopy
 qPCR
 sanders_11_ASD_discovery_cases
  White non-Hispanic, 74.5%; mixed, 9.3%, Asian, 4.3%, White Hispanic, 4.0%, African-American, 3.8%; other, 4.2&
 Solid phase hybridization
  Illumina 1M v1, Illumina 1M v3
 PennCNV, QuantiSNP, GNOSIS
 
 
 soueid_16_ASD_discovery_cases
  Lebanon
 Array SNP
  Affymetrix 2.7M, Affymetrix CytoScan
 
 Affymetrix ChAS
 None
 soueid_16_DD/ID_discovery_cases
  Lebanon
 Array SNP
  Affymetrix 2.7M, Affymetrix CytoScan
 
 Affymetrix ChAS
 None
 zhou_19_ASD_discovery_cases
  Han Chinese
 Targeted exome sequencing
  Roche NimbleGen SeqCap EZ Library, Illumina HiSeq 2500
 
 XHMM v.1.0
 qPCR

Controls

Cohort ID
Geographical Ancestry
Discovery Method
Platform
Algorithm
Software
Validation Method
  brandler_18_ASD_discovery_controls
  N/A
  WGS
  Illumina HiSeq X10 or HiSeq 2500
  ForestSV, Lumpy, Manta, Mobster, SV2
 
  None
  engchuan_15_ASD_discovery_controls
  Caucasian
  Solid phase hybridization
  Illumina 1M
 
 
  None
  krumm_15_ASD_discovery_controls
  N/A
  WES
 
  CoNIFER, XHMM
 
  Solid phase hybridization (Illumina 1M, 1 M Duo, or Omni 2.5)
  levy_11_ASD_discovery_controls
 
  aCGH
  NimbleGen HD2
  HMM
 
 
  prasad_12_ASD_discovery_controls
  NA
  aCGH
  Agilent 1M
  ADM-2, DNAcopy (R Bioconductor)
  DNA Analytics v4.0.85 (Agilent), DNAcopy
 
  sanders_11_ASD_discovery_controls
 
  Solid phase hybridization
  Illumina 1M v1 or Illumina 1M v3
  PennCNV, QuantiSNP, GNOSIS
 
 
  soueid_16_ASD_discovery_controls
  Lebanon
  Array SNP
  Affymetrix 2.7M, Affymetrix CytoScan
 
  Affymetrix ChAS
  None
  zhou_19_ASD_discovery_controls
  Han Chinese
  Targeted exome sequencing
  Roche NimbleGen SeqCap EZ Library, Illumina HiSeq 2500
 
  XHMM v.1.0
 

Cases

Patient ID
Author, Year
Age
Gender
Primary Diagnosis
Clinical Profile
Cognitive Profile
CNV Start
CNV End
CNV Size
Genome Build
Type Method
Validation
  brandler_18_ASD_replication_cases-case1-0367-003
 N/A
 M
 ASD
 Case from MSSNG cohort
 
 131495988
 131496703
  716
 GRCh38
 Deletion
 No
  brandler_18_ASD_replication_cases-caseAU2123301
 N/A
 M
 ASD
 Case from MSSNG cohort
 
 132145828
 132285602
  139775
 GRCh38
 Deletion
 No
  brandler_18_ASD_replication_cases-caseAU3853302
 N/A
 M
 ASD
 Case from MSSNG cohort
 
 131495988
 131496703
  716
 GRCh38
 Deletion
 No
  engchuan_15_ASD_discovery_cases-case3395_4
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 131917505
 132226472
  308968
 GRCh38
 Duplication
 No
  mosrati_12_ASD/MR_discovery_cases-caseV5
 26 yrs.
 M
 Autistic traits
 Behavioral and psychiatric evaluation: autistic traits reminiscent of Asperger syndrome. Language and communication evaluation: no oral speech; able to have coherent hand-sign conservation with mother and unaffected brother. Visual and auditory evaluation: moderate hearing loss. Family history: consanguineous parents; brother with autistic traits, mental retardation, and hearing loss; sister with mental retardation and hearing loss (no autistic traits).
 No mental retardation
 131123687
 131371175
  247488
 Unknown
 Deletion
 No
  prasad_12_ASD_discovery_cases-case59144
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. Novel CNV
 
 131972774
 131988294
  15521
 Unknown
 Duplication
 Yes
  prasad_12_ASD_discovery_cases-case69180
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. Novel CNV
 
 131704792
 131719045
  14254
 Unknown
 Deletion
 Yes
  prasad_12_ASD_discovery_cases-case88032
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. CNV identified by previous SNP microarray study
 
 132118051
 132230010
  111960
 Unknown
 Duplication
 No
  sanders_11_ASD_discovery_cases-11766.p1
 6
 M
 Autism
 NA
 Full-scale IQ, 104; non-verbal IQ, 107; verbal IQ, 96
 132089898
 132095496
  5599
 GRCh38
 Deletion
 No
  sanders_11_ASD_discovery_cases-12233.p1
 5.5
 M
 Autism
 NA
 Full-scale IQ, 106; non-verbal IQ, 108; verbal IQ, 99
 132089898
 132095496
  5599
 GRCh38
 Deletion
 No
  sanders_11_ASD_discovery_cases-12637.p1
 7.3
 M
 ASD
 NA
 Full-scale IQ, 105; non-verbal IQ, 110; verbal IQ, 96
 132089898
 132095496
  5599
 GRCh38
 Deletion
 No
  sanders_11_ASD_discovery_cases-13041.p1
 7
 M
 Autism
 NA
 Full-scale IQ, 98; non-verbal IQ, 102; verbal IQ, 93
 132089898
 132095496
  5599
 GRCh38
 Deletion
 No
  soueid_16_ASD_discovery_cases-caseSES2
 N/A
 M
 Autism
 Case fulfilled DSM-V criteria for autism; no other information available
 
 131745360
 132391573
  646214
 GRCh38
 Duplication
 No
  zhou_19_ASD_discovery_cases-caseAU048603
 N/A
 N/A
 ASD
 Diagnosis of ASD by ADI-R and ADOS.
 
 132145069
 132223691
  78623
 GRCh38
 Duplication
 Yes
  zhou_19_ASD_discovery_cases-caseAU049703
 N/A
 N/A
 ASD
 Diagnosis of ASD by ADI-R and ADOS.
 
 132159423
 132198686
  39264
 GRCh38
 Duplication
 Yes

Controls

Patient ID
Author, Year
Age
Gender
Primary Diagnosis
Clinical Profile
Cognitive Profile
CNV Start
CNV End
CNV Size
Genome Build
Type Method
Validation
  brandler_18_ASD_discovery_controls-controlSSC07271
  N/A
  M
  Control
  Control from SSC cohort
 
  132051245
  132052142
  898
  GRCh38
  Deletion
  No
  engchuan_15_ASD_discovery_controls-controlB627204_1007846383
  N/A
  N/A
  Control
  No previous psychiatric history
 
  131750610
  132394654
  644045
  GRCh38
  Duplication
  No
  engchuan_15_ASD_discovery_controls-controlHABC_901083_901083
  N/A
  N/A
  Control
  No previous psychiatric history
 
  131331332
  131547749
  216418
  GRCh38
  Duplication
  No
  krumm_15_ASD_discovery_controls-control11519.s1
  N/A
  Female
  Control
  Unaffected sibling from the Simons Simplex Collection (SSC)
 
  132377674
  132385295
  7622
  GRCh38
  Duplication
  Yes
  levy_11_ASD_discovery_controls-11519.s1
  NA
  F
  Control
  NA
  NA
  132365626
  132456929
  91304
  GRCh38
  Duplication
  No
  prasad_12_ASD_discovery_controls-control2
  NA
  NA
  Control
  NA
 
  131972774
  131988294
  15521
  Unknown
  Duplication
  No
  prasad_12_ASD_discovery_controls-control3
  NA
  NA
  Control
  NA
 
  131972774
  131988294
  15521
  Unknown
  Duplication
  No
  sanders_11_ASD_discovery_controls-11519.s1
  4.3
  F
  Control (matched sibling)
  NA
  NA
  132400020
  132454147
  54128
  GRCh38
  Duplication
  No
  sanders_11_ASD_discovery_controls-12060.s1
  10.6
  F
  Control (matched sibling)
  NA
  NA
  132089898
  132095496
  5599
  GRCh38
  Deletion
  No

Cases

Patient ID
Validation Description
Primary Disorder Inheritence
Inheritence
Family Profile
Disease Segregation
Gene Content
Altered Gene Expression
 brandler_18_ASD_replication_cases-case1-0367-003
 No validation step reported
 
 Maternal
 
 
 MKLN1
 
 brandler_18_ASD_replication_cases-caseAU2123301
 No validation step reported
 
 Maternal
 
 
 PLXNA4
 
 brandler_18_ASD_replication_cases-caseAU3853302
 No validation step reported
 
 Paternal
 
 
 MKLN1
 
 engchuan_15_ASD_discovery_cases-case3395_4
 
 
 Unknown
 
 
 PLXNA4
 
 mosrati_12_ASD/MR_discovery_cases-caseV5
 
 
 Unknown
 Multiplex
 Unknown
 0 genes
 
 prasad_12_ASD_discovery_cases-case59144
 qPCR
 
 Maternal
 Multiplex
 Not segregated (duplication present in unaffected sibling)
 PLXNA4
 
 prasad_12_ASD_discovery_cases-case69180
 qPCR
 
 Paternal
 Multiplex
 Segregated
 PLXNA4
 
 prasad_12_ASD_discovery_cases-case88032
 
 
 Unknown
 Simplex
 Unknown
 CHCHD3
 
 sanders_11_ASD_discovery_cases-11766.p1
 
 
 Paternal
 Simplex (quad-proband matched)
 Segregated
 
 
 sanders_11_ASD_discovery_cases-12233.p1
 
 
 Maternal
 Simplex (quad-proband matched)
 Segregated
 
 
 sanders_11_ASD_discovery_cases-12637.p1
 
 
 Paternal
 Simplex (quad-proband matched)
 Not segregated
 
 
 sanders_11_ASD_discovery_cases-13041.p1
 
 
 Both parents
 Simplex (quad-proband matched)
 Segregated
 
 
 soueid_16_ASD_discovery_cases-caseSES2
 
 
 Maternal
 Simplex
 
 NDUFB9P2,PLXNA4
 
 zhou_19_ASD_discovery_cases-caseAU048603
 qPCR
 
 Unknown
 
 
 PLXNA4
 
 zhou_19_ASD_discovery_cases-caseAU049703
 qPCR
 
 De novo
 
 
 PLXNA4
 

Controls

Patient ID
Validation Description
Primary Disorder Inheritence
Inheritence
Family Profile
Disease Segregation
Gene Content
Altered Gene Expression
brandler_18_ASD_discovery_controls-controlSSC07271
  Not available
 
  Unknown
 
 
 
 
engchuan_15_ASD_discovery_controls-controlB627204_1007846383
 
 
  Unknown
 
 
  NDUFB9P2,PLXNA4
 
engchuan_15_ASD_discovery_controls-controlHABC_901083_901083
 
 
  Unknown
 
 
  PODXL,MKLN1
 
krumm_15_ASD_discovery_controls-control11519.s1
  Illumina 1M
 
  Paternal
 
 
  PLXNA4
 
levy_11_ASD_discovery_controls-11519.s1
 
 
  Paternal
  Simplex
  NA
  PLXNA4
 
prasad_12_ASD_discovery_controls-control2
 
 
  Unknown
 
 
  PLXNA4
 
prasad_12_ASD_discovery_controls-control3
 
 
  Unknown
 
 
  PLXNA4
 
sanders_11_ASD_discovery_controls-11519.s1
 
 
  Paternal
  Simplex (quad)
  NA
  PLXNA4
 
sanders_11_ASD_discovery_controls-12060.s1
 
 
  Paternal
  Simplex (quad)
  NA
 
 

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