HELP     Sign In

17q23.2CNV Type: Deletion


Largest CNV size: 8418 bp

Statistics Box:
Number of Reports: 8



Summary Information

Summary statement in development

Additional Locus Information

Genome browsers

USCS Symbol             NCBI Symbol

Decipher

            Decipher Symbol

References

Major Reports

Title
Author, Year
Report Class
CNV Type
An evidence-based approach to establish the functional and clinical significance of copy number variants in intellectual and developmental disabili...
Deletion
Phenotypic heterogeneity of genomic disorders and rare copy-number variants.
Deletion-Duplication

Minor Reports

Title
Author, Year
Report Class
CNV Type
Novel copy number variants in children with autism and additional developmental anomalies.
Deletion
Multiple recurrent de novo CNVs, including duplications of the 7q11.23 Williams syndrome region, are strongly associated with autism.
Deletion
Novel candidate genes and regions for childhood apraxia of speech identified by array comparative genomic hybridization.
Deletion
A discovery resource of rare copy number variations in individuals with autism spectrum disorder.
Deletion
Performance of case-control rare copy number variation annotation in classification of autism.
Duplication
Functional analysis of TLK2 variants and their proximal interactomes implicates impaired kinase activity and chromatin maintenance defects in their pathogenesis
Deletion

Cases

Cohort ID
Author, Year
Descripton
Cohort Size
Diagnosis
Age
Gender
CNV Size
Deletion
Duplication
Total CNV's
 davis_09_ASD_discovery_cases
 Autistic cases from Autism Genetic Research Exchange (AGRE)
 36
 ASD: diagnosis confirmed through ADI and in some cases ADOS-G. 17 cases with syndromic autism (autism and less than common craniofacial dysmorphology, limb or digit abnormality, or ocular abnormality), 19 cases selected at random with autism and no associated syndromic features
 NA
 NA
 12603
 2
 0
 2
 engchuan_15_ASD_discovery_cases
 Samples from the Autism Genome Project (AGP)
 1892
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 N/A
 85.78% Male
 99104
 0
 1
 1
 girirajan_12_ASD/DD/ID_discovery_cases
 Samples from affected children submitted to Signature Genomic Laboratories from 2008-2010.
 32587
 Developmental delay with or without congenital malformations
 
 
 2020000
 6
 1
 7
 kaminsky_11_DD/ID/ASD_discovery_cases
 Cases from the International Standards for Cytogenomic Arrays (ISCA) consortium
 15749
 Unexplained developmental delay, intellectual disability, dysmorphic features, multiple congenital anomalies, autism spectrum disorders, or clinical features suggestive of a chromosomal syndrome
 NA
 NA
 1461167
 1
 0
 1
 laffin_12_CAS_discovery_cases
 Participants recruited and consented for a study of pediatric motor speech disorders
 24
 Diagnosis of childhood apraxia of speech (CAS) assessed by Madison Speech Assessment Protocol.
 Mean, 8.3 3.7 yrs.
 66% Male
 53144
 1
 0
 1
 pavinato_20_DD/ID_discovery_cases
 Patients from three families with TLK2 variants identified by screening of an in-house cohort of 736 patients with ASD and/or ID, a publically available cohort from the ASC (11,986 ASD cases), and the DECIPHER database
 6
 Affected individuals frequently presented with developmental delay and/or intellectual disability.
 Range, 3-47 yrs.
 50.0% Male
 38938
 1
 0
 1
 prasad_12_ASD_discovery_cases
 Unrelated ASD cases recruited from three Canadian sites (Hospital for Sick Children, McMaster University, and Memorial University of Newfoundland); the majority of cases had been previously genotyped with results published in Marshall et al., 2008 and Pinto et al., 2010. 20 cases from initial cohort of 696 were excluded from further analysis (due to CNVs > 5 Mb).
 676
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS
 NA
 82.84% Male
 9832
 3
 0
 3
 sanders_11_ASD_discovery_cases
 Autistic probands from the Simons Simplex Collection (SSC). 872 probands in quartet families, 272 probands in trios.
 1124
 ASD diagnosis: 89.5% autism; 8.5% PDD-NOS, 2% Asperger syndrome. Mean full-scale IQ 85.1 1.5 (mean verbal IQ, 81.9 1.7; mean non-verbal IQ, 88.4 1.4)
 Mean, 9.1 yrs.
 86.1% Male
 8418
 3
 0
 3

Controls

Cohort ID
Author, Year
Descripton
Cohort Size
Diagnosis
Age
Gender
CNV Size
Deletion
Duplication
Total CNV's
 engchuan_15_ASD_discovery_controls
 Platform-matched controls from three large studies: SAGE (Study of Addiction Genetics and Environment), Ontario Colorectal Cancer study, and HABC (Health Aging and Body Composition)
 2342
 Controls; subjects had no previous psychiatric history
 N/A
 46.67% Male
 92036
 1
 1
 2
 girirajan_12_ASD/DD/ID_discovery_controls
 Persons found to have no overt neurological disorders during screening for other studies
 8329
 Control
 
 
 2020000
 0
 0
 0
 kaminsky_11_DD/ID/ASD_discovery_controls
 Controls from the International Standards for Cytogenomic Arrays (ISCA) consortium
 10118
 Controls
 NA
 NA
 NA
 NA
 NA
 NA
 krumm_15_ASD_discovery_controls
 Unaffected siblings from quad families from the Simons Simplex Collection
 1786
 Control
 N/A
 N/A
 110337
 0
 1
 1
 prasad_12_ASD_discovery_controls
 PDx controls [1000 DNA samples from reportedly healthy donors (50.2% male) from BioServe (Beltsville, MD)] and 4139 in-house controls previously reported in Krawcak et al. 2006, Stewart et al. 2009, and Bierut et al. 2010. CNVs identified in controls were used to define rare ASD-specific CNVs.
 5139
 Control
 NA
 NA (PDx controls 50.2% male)
 9832
 0
 0
 0
 sanders_11_ASD_discovery_controls
 Matched siblings of autistic probands from the Simons Simplex Collection (SSC).
 872
 Controls
 Mean, 10.0 yrs.
 
 10193
 1
 0
 1

Cases

Cohort ID
Geographical Ancestry
Discovery Method
Platform
Algorithm
Software
Validation Method
 davis_09_ASD_discovery_cases
  NA
 Array SNP
  Affymetrix 250K Nsp, Affymetrix 250K Syt
 HMM
 CNAG v2.0
 None
 engchuan_15_ASD_discovery_cases
  Caucasian
 Solid phase hybridization
  Illumina 1M
 
 
 None
 girirajan_12_ASD/DD/ID_discovery_cases
 
 aCGH
  BACs aCGH, SignatureChipOS
 
 
 FISH, aCGH, or confirmation by inheritance
 kaminsky_11_DD/ID/ASD_discovery_cases
  NA
 aCGH
  Agilent 44K, Agilent 105K
 
 Feature Extraction, DNA Analytics
 FISH, qPCR, MLPA, aCGH, standard G-banded chromosome analysis
 laffin_12_CAS_discovery_cases
  NA
 aCGH
  Customized 385K NimbleGen array with increased coverage of genes & regions previously associated with CAS
 
 OGT CytoSure Interpret v.3.4.3
 None
 pavinato_20_DD/ID_discovery_cases
  Caucasian
 aCGH
  Agilent 60K
 
 
 None
 prasad_12_ASD_discovery_cases
  Canada
 aCGH
  Agilent 1M
 ADM-2, DNAcopy (R Bioconductor)
 DNA Analytics v4.0.85 (Agilent), DNAcopy
 None
 sanders_11_ASD_discovery_cases
  White non-Hispanic, 74.5%; mixed, 9.3%, Asian, 4.3%, White Hispanic, 4.0%, African-American, 3.8%; other, 4.2&
 Solid phase hybridization
  Illumina 1M v1, Illumina 1M v3
 PennCNV, QuantiSNP, GNOSIS
 
 

Controls

Cohort ID
Geographical Ancestry
Discovery Method
Platform
Algorithm
Software
Validation Method
  engchuan_15_ASD_discovery_controls
  Caucasian
  Solid phase hybridization
  Illumina 1M
 
 
  None
  girirajan_12_ASD/DD/ID_discovery_controls
 
  aCGH
  BACs ACGH (SignatureChipoWG) or oligoarray (SignatureChipOS)
 
 
 
  kaminsky_11_DD/ID/ASD_discovery_controls
  NA
  aCGH
  Agilent 44K, Agilent 105K
 
  Feature Extraction, DNA Analytics
 
  krumm_15_ASD_discovery_controls
  N/A
  WES
 
  CoNIFER, XHMM
 
  Solid phase hybridization (Illumina 1M, 1 M Duo, or Omni 2.5)
  prasad_12_ASD_discovery_controls
  NA
  aCGH
  Agilent 1M
  ADM-2, DNAcopy (R Bioconductor)
  DNA Analytics v4.0.85 (Agilent), DNAcopy
 
  sanders_11_ASD_discovery_controls
 
  Solid phase hybridization
  Illumina 1M v1 or Illumina 1M v3
  PennCNV, QuantiSNP, GNOSIS
 
 

Cases

Patient ID
Author, Year
Age
Gender
Primary Diagnosis
Clinical Profile
Cognitive Profile
CNV Start
CNV End
CNV Size
Genome Build
Type Method
Validation
  davis_09_ASD_discovery_cases-AU038703
 NA
 NA
 Non-syndromic ASD
 Diagnosis: broad spectrum autism. Non-syndromic autism (no craniofacial dysmorphology, limb or digit malformation, or ocular abnormality).
 
 51510249
 51520028
  9779
 Unknown
 Deletion
 No
  davis_09_ASD_discovery_cases-AU057905
 NA
 NA
 Non-syndromic ASD
 Diagnosis: broad spectrum autism. Non-syndromic autism (no craniofacial dysmorphology, limb or digit malformation, or ocular abnormality).
 
 51510249
 51522852
  12603
 Unknown
 Deletion
 No
  engchuan_15_ASD_discovery_cases-case3481_3
 N/A
 N/A
 ASD
 Diagnosis of ASD based on Autism Diagnostic Observation Schedule (ADOS) and Autism Diagnostic Interview-Revised (ADI-R)
 
 60352936
 60452040
  99105
 GRCh38
 Duplication
 No
  girirajan_12_ASD/DD/ID_discovery_cases-case1534
 NA
 NA
 Developmental delay
 NA
 NA
 60207857
 62227857
  2020001
 GRCh38
 Deletion
 NA
  girirajan_12_ASD/DD/ID_discovery_cases-case1535
 NA
 NA
 Developmental delay
 NA
 NA
 60207857
 62227857
  2020001
 GRCh38
 Deletion
 NA
  girirajan_12_ASD/DD/ID_discovery_cases-case1536
 NA
 NA
 Developmental delay
 NA
 NA
 60207857
 62227857
  2020001
 GRCh38
 Deletion
 NA
  girirajan_12_ASD/DD/ID_discovery_cases-case1537
 NA
 NA
 Developmental delay
 NA
 NA
 60207857
 62227857
  2020001
 GRCh38
 Deletion
 NA
  girirajan_12_ASD/DD/ID_discovery_cases-case1538
 NA
 NA
 Developmental delay
 NA
 NA
 60207857
 62227857
  2020001
 GRCh38
 Deletion
 NA
  girirajan_12_ASD/DD/ID_discovery_cases-case1539
 NA
 NA
 Developmental delay
 NA
 NA
 60207857
 62227857
  2020001
 GRCh38
 Deletion
 NA
  girirajan_12_ASD/DD/ID_discovery_cases-case1540
 NA
 NA
 Developmental delay
 NA
 NA
 60207857
 62227857
  2020001
 GRCh38
 Duplication
 NA
  kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00001145
 NA
 NA
 Developmental delay/intellectual disability/ASD
 Clinical profile NA
 Cognitive profile NA
 60857298
 62318465
  1461168
 GRCh38
 Deletion
 Yes
  laffin_12_CAS_discovery_cases-case12
 10-15 yrs.
 NA
 CAS
 Years of apraxia treatment: 10. Familial status: positive (one or more nuclear family members with a verbal trait disorder including speech disorder, language disorder, reading disorder, cognitive disability, or learning disability). Language impairment: none. Motor impairment: none.
 No cognitive impairment
 57315787
 57368931
  53145
 GRCh38
 Deletion
 No
  pavinato_20_DD/ID_discovery_cases-caseFam3-p6
 16 yrs.
 F
 Developmental delay
 Birth/neonatal history: premature birth (35 weeks), small for gestational age (birth weight -2.10 SD), birth length less than 3rd percentile (height 1st %ile). Developmental milestones: delayed motor development. Motor and musculoskeletal evaluation: skeletal anomalies of the hands (absence of flexure fold of the thumbs, short hands with inability to bend thumbs, short and brittle nails). Additional medical history: persistent arterial canal, feeding difficulties. Dysmorphic features: slightly short forehead, hypertelorism, large nasal root, epicanthus, bifid nasal tip, absent earlobes, narrow and upslanted palpebral fissures. Growth parameters: underweight (BMI 17.9 at 17 years).
 Difficulties in memory and transcription
 62606100
 62645037
  38938
 GRCh38
 Deletion
 No
  prasad_12_ASD_discovery_cases-case63582-L
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. Novel CNV
 
 56212732
 56222563
  9832
 Unknown
 Deletion
 No
  prasad_12_ASD_discovery_cases-case83553L
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. Novel CNV
 
 56212732
 56222563
  9832
 Unknown
 Deletion
 No
  prasad_12_ASD_discovery_cases-case91617
 NA
 M
 ASD
 Diagnosis of ASD based on meeting criteria on ADI-R and/or ADOS. Novel CNV
 
 56212732
 56222563
  9832
 Unknown
 Deletion
 No
  sanders_11_ASD_discovery_cases-11121.p1
 10.3
 M
 Autism
 NA
 Full-scale IQ, 102; non-verbal IQ, 103; verbal IQ, 99
 62916947
 62925365
  8419
 GRCh38
 Deletion
 No
  sanders_11_ASD_discovery_cases-12252.p1
 7.2
 M
 Autism
 NA
 Full-scale IQ, 87; non-verbal IQ, 79; verbal IQ, 106
 61042000
 61047056
  5057
 GRCh38
 Deletion
 No
  sanders_11_ASD_discovery_cases-13367.p1
 9.7
 F
 Autism
 NA
 Full-scale IQ, 53; non-verbal IQ, 57; verbal IQ, 46
 61330689
 61333241
  2553
 GRCh38
 Deletion
 No

Controls

Patient ID
Author, Year
Age
Gender
Primary Diagnosis
Clinical Profile
Cognitive Profile
CNV Start
CNV End
CNV Size
Genome Build
Type Method
Validation
  engchuan_15_ASD_discovery_controls-controlB531891_1007854698
  N/A
  N/A
  Control
  No previous psychiatric history
 
  61467355
  61502720
  35366
  GRCh38
  Deletion
  No
  engchuan_15_ASD_discovery_controls-controlHABC_901248_901248
  N/A
  N/A
  Control
  No previous psychiatric history
 
  61738555
  61830591
  92037
  GRCh38
  Duplication
  No
  krumm_15_ASD_discovery_controls-control14008.s1
  N/A
  Male
  Control
  Unaffected sibling from the Simons Simplex Collection (SSC)
 
  61952964
  62063301
  110338
  GRCh38
  Duplication
  Yes
  sanders_11_ASD_discovery_controls-11135.s1
  12.9
  F
  Control (matched sibling)
  NA
  NA
  62915172
  62925365
  10194
  GRCh38
  Deletion
  No

Cases

Patient ID
Validation Description
Primary Disorder Inheritence
Inheritence
Family Profile
Disease Segregation
Gene Content
Altered Gene Expression
 davis_09_ASD_discovery_cases-AU038703
 
 
 Unknown
 Unknown
 Unknown
 0 genes
 
 davis_09_ASD_discovery_cases-AU057905
 
 
 Unknown
 Unknown
 Unknown
 0 genes
 
 engchuan_15_ASD_discovery_cases-case3481_3
 
 
 Unknown
 
 
 RPL12P38,APPBP2,USP32,C17orf64
 
 girirajan_12_ASD/DD/ID_discovery_cases-case1534
 NA
 
 Unknown
 Unknown
 Unknown
 SCARNA20,RPL12P38,RPSAP66,RNU6-623P,RN7SL606P,KRT18P61,HMGN1P28,RN7SL448P,RPL23AP74,C17orf82,NACA2,RN7SL800P,POLRMTP1,APPBP2,LINC01999,PPM1D,TBX2-AS1,TBX2,USP32,C17orf64,TBX4,BRIP1,MED13,BCAS3,INTS2
 
 girirajan_12_ASD/DD/ID_discovery_cases-case1535
 NA
 
 Unknown
 Unknown
 Unknown
 SCARNA20,RPL12P38,RPSAP66,RNU6-623P,RN7SL606P,KRT18P61,HMGN1P28,RN7SL448P,RPL23AP74,C17orf82,NACA2,RN7SL800P,POLRMTP1,APPBP2,LINC01999,PPM1D,TBX2-AS1,TBX2,USP32,C17orf64,TBX4,BRIP1,MED13,BCAS3,INTS2
 
 girirajan_12_ASD/DD/ID_discovery_cases-case1536
 NA
 
 Unknown
 Unknown
 Unknown
 SCARNA20,RPL12P38,RPSAP66,RNU6-623P,RN7SL606P,KRT18P61,HMGN1P28,RN7SL448P,RPL23AP74,C17orf82,NACA2,RN7SL800P,POLRMTP1,APPBP2,LINC01999,PPM1D,TBX2-AS1,TBX2,USP32,C17orf64,TBX4,BRIP1,MED13,BCAS3,INTS2
 
 girirajan_12_ASD/DD/ID_discovery_cases-case1537
 NA
 
 Unknown
 Unknown
 Unknown
 SCARNA20,RPL12P38,RPSAP66,RNU6-623P,RN7SL606P,KRT18P61,HMGN1P28,RN7SL448P,RPL23AP74,C17orf82,NACA2,RN7SL800P,POLRMTP1,APPBP2,LINC01999,PPM1D,TBX2-AS1,TBX2,USP32,C17orf64,TBX4,BRIP1,MED13,BCAS3,INTS2
 
 girirajan_12_ASD/DD/ID_discovery_cases-case1538
 NA
 
 Unknown
 Unknown
 Unknown
 SCARNA20,RPL12P38,RPSAP66,RNU6-623P,RN7SL606P,KRT18P61,HMGN1P28,RN7SL448P,RPL23AP74,C17orf82,NACA2,RN7SL800P,POLRMTP1,APPBP2,LINC01999,PPM1D,TBX2-AS1,TBX2,USP32,C17orf64,TBX4,BRIP1,MED13,BCAS3,INTS2
 
 girirajan_12_ASD/DD/ID_discovery_cases-case1539
 NA
 
 Unknown
 Unknown
 Unknown
 SCARNA20,RPL12P38,RPSAP66,RNU6-623P,RN7SL606P,KRT18P61,HMGN1P28,RN7SL448P,RPL23AP74,C17orf82,NACA2,RN7SL800P,POLRMTP1,APPBP2,LINC01999,PPM1D,TBX2-AS1,TBX2,USP32,C17orf64,TBX4,BRIP1,MED13,BCAS3,INTS2
 
 girirajan_12_ASD/DD/ID_discovery_cases-case1540
 NA
 
 Unknown
 Unknown
 Unknown
 SCARNA20,RPL12P38,RPSAP66,RNU6-623P,RN7SL606P,KRT18P61,HMGN1P28,RN7SL448P,RPL23AP74,C17orf82,NACA2,RN7SL800P,POLRMTP1,APPBP2,LINC01999,PPM1D,TBX2-AS1,TBX2,USP32,C17orf64,TBX4,BRIP1,MED13,BCAS3,INTS2
 
 kaminsky_11_DD/ID/ASD_discovery_cases-ISCA00001145
 FISH, qPCR, MLPA, aCGH, or standard G-banded chromosome analysis
 
 Unknown
 Unknown
 Unknown
 RN7SL448P,RPL23AP74,C17orf82,NACA2,RN7SL800P,POLRMTP1,TBX2-AS1,TBX2,TBC1D3P2,TBX4,BRIP1,MED13,BCAS3,INTS2
 
 laffin_12_CAS_discovery_cases-case12
 
 
 Unknown
 Multiplex
 Unknown
 MSI2
 
 pavinato_20_DD/ID_discovery_cases-caseFam3-p6
 
 
 De novo
 Simplex
 
 MRC2,TLK2
 Patient fibroblasts showed approximately 50% reduction in TLK2 mRNA expression.
 prasad_12_ASD_discovery_cases-case63582-L
 
 
 Unknown
 Unknown
 Unknown
 BCAS3
 
 prasad_12_ASD_discovery_cases-case83553L
 
 
 Unknown
 Unknown
 Unknown
 BCAS3
 
 prasad_12_ASD_discovery_cases-case91617
 
 
 Unknown
 Simplex
 Segregated
 BCAS3
 
 sanders_11_ASD_discovery_cases-11121.p1
 
 
 Unknown
 Simplex (quad-proband matched)
 Segregated
 
 
 sanders_11_ASD_discovery_cases-12252.p1
 
 
 Maternal
 Simplex (quad-proband matched)
 Segregated
 BCAS3
 
 sanders_11_ASD_discovery_cases-13367.p1
 
 
 Paternal
 Simplex (trio)
 NA
 BCAS3
 

Controls

Patient ID
Validation Description
Primary Disorder Inheritence
Inheritence
Family Profile
Disease Segregation
Gene Content
Altered Gene Expression
engchuan_15_ASD_discovery_controls-controlB531891_1007854698
 
 
  Unknown
 
 
  TBX4
 
engchuan_15_ASD_discovery_controls-controlHABC_901248_901248
 
 
  Unknown
 
 
  BRIP1
 
krumm_15_ASD_discovery_controls-control14008.s1
  Omni2.5-4v1
 
  Paternal
 
 
  RN7SL800P,MED13
 
sanders_11_ASD_discovery_controls-11135.s1
 
 
  Unknown
  Simplex (quad)
  NA
 
 

No Animal Model Data Available
HELP
Copyright © 2017 MindSpec, Inc.